Retroperitoneal composite pheochromocytomaganglioneuroma. Retroperitoneal neoplasms are rare and easily misdiagnosed. Proton or photon rt for retroperitoneal sarcomas full. Hello all my wife had been diagnosed with ovarian cancer in january 2012 stage 2a she had hysterectomy followed by chemotherapy carbotaxol she had recurrence on june 20 in an lymph node near ivc. We report a case of a 42 year old female presenting with abdominal pain who had a retroperitoneal tumour situated at the aortic bifurcation. Primary retroperitoneal neurofibroma that mimics a. Any information contained in this pdf file is automatically generated from. Retroperitoneal space, kidneys, ureters flashcards. Preoperative diagnosis helps to plan treatment and prevent complications. Click, drag, and drop to reorder files or press delete to remove any content you dont want. To change the order of your pdfs, drag and drop the files as you want. Large retroperitoneal paraganglioma concurrent with.
Neuroblatoma a common retroperitoneal tumor in children vijay khajuria neuroblastoma are solid extracranial tumors that commonly affects children. Testicular carcinoma is the most common urologic indication for rplnd, followed by renal cell carcinoma and upper urinary tract urothelial carcinoma. Retroperitoneal space an overview sciencedirect topics. We report a case of a 42 year old female presenting with abdominal pain who had a retroperitoneal tumour situated at. Experience at a north indian tertiary care center santosh kumar1, gautam ram choudhary1, shivanshu singh1, seema prasad2, shrawan kumar singh1, anil bhansali3, sanjay bhadada3, pinaki dutta3. Clinically and histologically, these tumors are similar pancreatic and ovarian mucinous. Since retroperitoneal paragangliomas are rare, the behavior and treatment outcomes of this type of tumor remain unclear. Us retroperitoneal complete img493 longitudinal images to include lateral, mid, and medial images of both kidneys. Click add files and select the files you want to include in your pdf. Radioanatomy of the retroperitoneal space emconsulte. Retroperitoneal paragangliomas are mostly benign with good. Over time, it can lead to a mass behind the abdomen called retroperitoneal fibrosis.
Download fulltext pdf download fulltext pdf composite paragangliomaganglioneuroma in the retroperitoneum article pdf available in world journal of surgical oncology 71. Minimal access retroperitoneal pancreatic necrosectomy. Proton or photon rt for retroperitoneal sarcomas the safety and scientific validity of this study is the responsibility of the study sponsor and investigators. Retroperitoneal tumors rts develop insidiously and are generally seen as large masses, and 50% of rts are larger than 20 cm at the time of diagnosis. Retroperitoneal fluid fluid is generally anechoic but may contain a variable number of echoes depending on the presence of cells, debris andor gas bubbles. The imaging characteristics of peripheral pnets are nonspecific. Gross pathology the mass already bisected in two different containers measuring 9x6. Paragangliomas are rare with multicentricity being more common in patients with familial history. A useful mnemonic to remember which organs are retroperitoneal is. Retroperitoneal paraganglioma with metastasis to the. Basic clinical retroperitoneal anatomy for pelvic surgeons ncbi. Teratoma is a germ cell tumor that originates from pluripotent germ cells.
Only 4 cases in the retroperitoneum have been described in the online database pubmed. Childhood cancer in the united states is the leading cause of death in children of 1 to 15 years age 1. The recurrence rate for patients with a median followup of 2 years was 14%, eliminating patients with followup times less than 1. You can merge pdfs or a mix of pdf documents and other files. Learn vocabulary, terms, and more with flashcards, games, and other study tools. Organs are retroperitoneal if they only have peritoneum on their anterior side.
Your story matters citation xu, weifeng, hanzhong li, zhigang ji, weigang yan, yushi zhang, xuebin zhang, and qian li. A 57yearold male complained of back pain and microhematuria. We are presenting prospective study of retroperitoneal tumours five tumours included in study carried out during two years at department of paed. Cancerous forms represent 20%50% of cases and are characterized by the occurrence of ganglionic or distant metastases in 30% of cases. Retroperitoneal paraganglioma manifesting as paralytic. Paragangliomas are tumors that arise from extraadrenal medullary neural crest derivatives. When presenting within the abdominal cavity, they may arise as a primary retroperitoneal neoplasm and can mimic vascular malformations or other conditions related to specific retroperitoneal organs such as the pancreas, kidneys, or. Extraadrenal paraganglioma of the retroperitoneum with metastasis to the vertebra is very rare. Retroperitoneal lymph node dissection rplnd has a diagnostic and therapeutic role in many urologic malignancies. The patient 60 yr old female non diabetic and non hypertensive known case of cva 7 yrs back with left hemiparesis and tobacco chewer presented with complains of pain in abdomen and vomiting since 5 days associated with increased sweating, facial flushing, nausea and. Peripheral primitive neuroectodermal tumors ppnet tend to be large and aggressive retroperitoneal tumors. A rare cause of high intestinal obstruction article pdf available in pan african medical journal 18.
The diagnosis of fat in a tumor on ct is based on its low density which is identical to that of subcutaneous, peritoneal, or retroperitoneal fat by visual inspection. A case of solitary neurofibroma in the retroperitoneum involving the uncinate process of the pancreas, which has been reported in only one case in japan and less than 20 cases in the world literature, is described. Partial nephrectomy is the standard treatment for small renal masses. Large retroperitoneal mass in a young female patient. Both lpn and rpn can be performed through transperitoneal tp or retroperitoneal rp approach. Retroperitoneal ganglioneuroma gn is a type of benign neurogenic tumor that originates from the retro peritoneal sympathetic. The most common retroperitoneal sarcoma is liposarcoma. How to merge pdfs and combine pdf files adobe acrobat dc. Longitudinal, ap, and transverse measurements of both kidneys. Transverse images to include superior, mid, and inferior of both kidneys. Survival of patients undergoing resection of retroperitoneal paraganglioma stratified by a size, b functional status, c margin status, and d nodal status. Retroperitoneal paragangliomas are mostly benign with.
A case of neurofibroma located in the retroperitoneum. An 81yearold woman was admitted with progressive abdominal fullness. Primary neuroendocrine tumor of the retroperitoneum. Clinical presentation and treatment outcomes in two patients. Any information contained in this pdf file is automatically generated from digital. Case report complete resection of a gigantic ganglioneuroma in. On computed tomography ct, a retroperitoneal tumor containing fat and soft tissue parts suggests a diagnosis of a retroperitoneal liposarcoma 1, 2. In 60% of cases, they secrete hormones and are classified as pheochromocytomas. To determine whether mri feature analysis can differentiate benign retroperitoneal extraadrenal paragangliomas and schwannomas. The paraganglioma is a rare tumor associated with high morbidity and mortality when the diagnosis is made intraoperatively. An 18yearold, unmarried woman presented with pain and progressively increasing swelling in right side of the abdomen of 4 months duration. The retroperitoneum is deep in the abdomen and pelvis, behind the abdominal lining. The retroperitoneal space is in front of the lower back and behind the abdominal lining peritoneum. Retroperitoneal tumors and pelvic floor hernias are rare clinical entities.
Paragangliomas are rare neoplasms arising from cells of the primitive neural crest. Download fulltext pdf download fulltext pdf composite paragangliomaganglioneuroma in the retroperitoneum article pdf available in world journal of. Retroperitoneal organs mnemonic radiology reference article. Their proximity to vital structures especially vascular makes resection difficult. Early recognition of the characteristic symptoms of headache, palpitations, and diaphoresis in a patient with hypertension and prompt appropriate intervention can minimize the morbidity associated with such tumors and prevent a potentially fatal outcome. Merge pdf files combine pdfs in the order you want with the easiest pdf merger available. Ctabdomenreveals retroperitoneal mass arise below the body and tail of pancreas and anterior to the left kidney. Retroperitoneal topographic anatomy, retroperitoneal vasculature, ureteric dissection and pelvic avascular spaces are the precise points during. Less than 10% of teratomas are found in the retroperitoneum.
Care should be undertaken not to prematurely diagnose either of these conditions. However, tumor invasion of the ivc is also seen in cancers of the kidney, adrenal, liver, and uterus. Is essential to rule out the existence of paraganglioma in all retroperitoneal tumors, even in asymptomatic and hemodynamically stable patients. In this article, we share our experience of 5 years of surgical management of rts. Retroperitoneal fibrosis rpf is characterized by the development of extensive fibrosis throughout the retroperitoneum, typically centered over the anterior surface of the fourth and fifth lumbar vertebrae and resulting in entrapment and obstruction of retroperitoneal structures, notably the ureters. Workup included history and physical exam, imaging, biopsy, colonoscopy, and gynecologic exam. However, they should be considered in the differential diagnosis of a large, aggressive retroperitoneal mass. The retroperitoneal space may be imaged from a ventral abdominal or flank approach. Pdf paragangliomas are rare neoplasms arising from cells of the primitive neural crest. Symptoms of retroperitoneal sarcomas can vary depending on the size and. After surgical resection, the mass was determined to be a primary retroperitoneal mucinous tumor prmt. Case note retroperitoneal nonfunctioning paraganglioma p aragangliomas are extraadrenal chromaffin tumours1 that develop at the expense of neuroectodermal cells of the autonomous nervous system.
The evolution of minimally invasive partial nephrectomy led to widespread utilization of laparoscopic lpn and robotic partial nephrectomy rpn. Visible mass occupying the epigastric and left lumbar region. An unusual retroperitoneal mass non functioning retroperitoneal paraganglioma 2 of 4 figure 1 figure. Minimal access retroperitoneal pancreatic necrosectomy improvement in morbidity and mortality with a less invasive approach. Please, select more pdf files by clicking again on select pdf files. Retroperitoneal paragangliomas mainly affect adults who are in the fourth or fifth decade of life, and they have no sex predilection 2. The full text of this article is available in pdf format. Management of patients with retroperitoneal tumors and a. Primary retroperitoneal paraganglioma simulating a. Paragangliomas are extraadrenal tumors of the autonomic nervous system and may be found within the skull base, neck, chest, and abdomen. Clinically, patients with a retroperitoneal paraganglioma often present with back pain or a palpable mass. There was an upper paramedian, left sided, large, palpable mass on the physical examination. Retroperitoneal leiomyosarcoma is characteristically large, nonfatty, and extensively necrotic, with a propensity for intravascular extensions.
Retroperitoneal inflammation causes swelling that occurs in the retroperitoneal space. These tumours are often difficult to diagnose and treat. Teratoma is the third most common tumor in the retroperitoneum in children, after neuroblastoma and wilms tumor. A rare case of retroperitoneal ganglioneuroma incidentally found during an annual health examination is presented.
We evaluated 28 rt cases operated on in three education hospitals in turkey from january 2008 onwards, with regard to patients. These tumors are often discovered incidentally during imaging studies performed for other reasons. Retroperitoneal schwannoma also termed neurilemmomas or neurinomas is a rare entity comprising only 0. Rearrange individual pages or entire files in the desired order.
Diagnosis and surgical treatment of retroperitoneal. Retroperitoneal laparoscopic management of paraganglioma. Peripheral primitive neuroectodermal tumor radiology. A single institute experience the harvard community has made this article openly available. Adrenal glands kidneys ureter bladder aorta inferior vena cava esophagus rectum uterus secondarily retroperitoneal. Some features of this site may not work without it. Laboratory investigations showed an increase in liver enzyme levels. Physical examination and routine laboratory studies gave normal results. The exact incidence of retroperitoneal paragangliomas is unknown, although males are typically affected more frequently than females. Here, we present an oroginal case of paraganglioma of the retroperitoneum with metastasis to the abdominal vertebra in a 42yearold female patient who was successfully. Listing a study does not mean it has been evaluated by the u.
Retroperitoneal space, kidneys, crosssectional anatomy. They are usually located in the head and neck but can be found in various body sites, including the. Most were located in the adrenal glands, and extraadrenal composite pheochromocytoma is extremely rare. They account for nearly 810% of all cancers in children and arise from undifferenciated neural crest precursor cells that differentiate into sympathetic nervous system. Majority of cancers in children are malignant solid tumours and about 4000 new cases are diagnosed each year 2. The retroperitoneal space has well defined anterior and posterior limits. Incidental retroperitoneal paraganglioma, general anaesthesia challenges. Neuroblatoma a common retroperitoneal tumor in children.
Transperitoneal vs retroperitoneal laparoscopic or robotic. Multiple retroperitoneal paragangliomas springerlink. Spectrum of retroperitoneal and genitourinary paraganglioma. In addition, most patients are diagnosed between 30 and 45 years of age andersen et al. To our knowledge this is the first report of this kind of disease in the literature.
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